Idiopathic subglottic stenosis in a patient with generalized port-wine stain (PWS): A case report and review of literature

  • Elham Behrangi Dermatology Department, Rasoul Akram Hospital, Iran University Of Medical Sciences, Tehran, Iran
  • Laya Yousefian Otolaryngology Department, Rasoul Akram Hospital, Iran University Of Medical Sciences, Tehran, Iran
  • Aliakbar Moodi Otolaryngologist, Ziaiyan Hospital, Tehran University of Medical Sciences, Tehran, Iran
  • Zahra Azizian Dermatology Department, Rasoul Akram Hospital, Iran University Of Medical Sciences, Tehran, Iran
DOI: https://doi.org/10.31661/gmj.v4i2.292
Keywords: port-wine stain (PWS), subglottic stenosis, vascular malformation

Abstract

Background: Subglottic stenosis is defined as inflammatory narrowing of the airway. It can be related to trauma, intubation, autoimmune disorders, vascular malformations, infection and congenital abnormalities. Pot-Wine Stain (PWS) is a small dermis venous malformation which is present at birth. PWS is found on face and neck, but can occur in throat and can cause subglottic stenosis. Case Report: Authors describe an 18-year-old girl with progressive dyspnea misdiagnosed with asthma having no response to medication. She has no histories of trauma, intubation, gastro-esophageal reflux disease (GERD) or allergy symptoms. Conclusion: Evaluations revealed subglottic stenosis in association with generalized PWS. To the best of our knowledge, this finding has not been reported in English medical literature. [GMJ.2015;4(2):126-28]

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Published
2015-03-16
How to Cite
Behrangi, E., Yousefian, L., Moodi, A., & Azizian, Z. (2015). Idiopathic subglottic stenosis in a patient with generalized port-wine stain (PWS): A case report and review of literature. Galen Medical Journal, 4(2), 126-28. https://doi.org/10.31661/gmj.v4i2.292
Issue
Vol. 4 No. 2 (2015): June 2015
Section
Case Report/Series

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